Curriculum · Pediatric / Nutrition & Growth / EPI / Routine Child Examination
Cyanotic congenital heart disease
What it is
The classification of congenital heart disease has two groups. The group that is not cyanotic holds the left to right shunt group (ASD, VSD, PDA) and the outflow obstruction group (AS, PS, coarctation of aorta). The cyanotic group holds tetralogy of Fallot and transposition of the great vessels; tricuspid regurgitation and total anomalous pulmonary venous connection are also named among the cyanotic heart diseases of infancy. Tetralogy of Fallot is the most common form of cyanotic congenital heart disease. Its four parts are pulmonary stenosis, VSD, overriding aorta and right ventricular hypertrophy, and the degree of right ventricular outflow obstruction sets how bad the disease is. In tricuspid atresia the absence of the tricuspid valve results in a hypoplastic right ventricle, so all systemic venous return must cross the atrial septum into the left atrium, and a PDA or VSD is necessary for pulmonary blood flow and survival. The named cyanotic lesions also include aortic atresia, D-transposition of the great arteries, hypoplastic left heart syndrome, L-transposition of the great arteries, persistent pulmonary hypertension of the newborn, pulmonary atresia with intact ventricular septum, total anomalous pulmonary venous connection and tricuspid atresia.